Sickle Cell Disease - A Case Report


  • Samarpita Pramanik, R.N. R.M. MSc (N) Department of Nursing, Christian Hospital Berhampur (CHB), Odisha, India



Sickle cell Disease, Sickle cell pain, Acute chest syndrome, Haemolytic Anaemia.


Sickle cell disease (SCD) is a major healthcare and societal problem affecting millions of people worldwide. In United States of America (USA), it is the most common genetic disorder affecting more than 80,000 people per year; majority of which are the African Americans Arabian and Indian. It is a genetic blood disorder affecting the red blood cells. Sickle cell pain is the hallmark of sickle cell disease and is associated with a very high mortality and morbidity rates. Being a genetic abnormality, the complete eradication of the disease from the affected seems to be difficult. Genetic counselling during pregnancy being the prime preventive step, Hematopoietic stem cell transplantation becomes the mainstay of treatment for complete eradication of the disease. But it is not done very often because of the significant risks involved.


Balgir RS, Sharma SK. Distribution of sickle cell haemoglobin in India. Indian J Hematol 1988;6:1-14.

Colah R, Mukherjee M, Ghosh K. Sickle cell disease in India. Curr Opin Hematol 2014;21:215-23.

Kleigmian K. Nelson Textbook of Pediatrics. 1st ed. Philadelphia, PA: Saunders; 2007. p. 2027-30.

Lehmann H, Cutbush M. Sickle-cell trait in southern India. Br Med J 1952;1:404-5.

Government of Gujarat. Sickle Cell Anemia Control Project. Ahmedabad: Government of Gujarat; 2012. Available from: https:// [Last accessed on 2021 Jan 03].

Mulumba LL, Wlson L. Sickle cell disease among children in Africa: An integreative literature review and global recommendations. Int J Afr

Nurs Sci 2015;3:56-64.

Pedram M, Jaseeb K, Haghi S, Vafaie M. First presentation of sickle cell anemia in a 35 year old girl: case report. Iran Red Crescent Med J


Rao VR. Genetics and Epidemiology of sickle cell anemia in India. Indian J Med Sci 1988;42:218-22.

Deepak S, Yasobant S, Golechha M. Situational analysis of sickle cell disease in Gujarat, India. Indian J Community Med 2017;42:218-22.

Seeler RA, Shwiaki MZ. Acute Splenic Sequestration crisis in young children with sickle cell anemia. Clinical observation in 20 episodes in

children. Clin Pediatr (Phila) 1972;11:701-4.

Serjeant GR, Ghosh K, Patel J. Sickle cell disease in India: A perspective. Indian J Med Res 2016;143:21-4.

Wethers DL. Sickle cell disease in children: Part II. Diagnosis and treatment of major complications and recent advances in treatment.

Am Fam Pysicians 2000;62:1309-14.




How to Cite

Samarpita Pramanik, R.N. R.M. MSc (N). (2021). Sickle Cell Disease - A Case Report. Asian Pacific Journal of Nursing and Health Sciences, 4(2), 1–4.